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KMID : 0378019730160050045
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New Medical Journal
1973 Volume.16 No. 5 p.45 ~ p.50
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Clinical Studies of Duchenne Type Muscular Dystrophy
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文亨南/Moon, Hyung Nam
申延淳/鄭仁熙/Shin, Jung Soon/Chung, In Hee
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Abstract
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From March, 1972 to March, 1973, fifteen patients with Duchenne type muscular dystrophy were examined for the electromyographic studies at Severance Hospital.
Duchenne type muscular dystrophy is a hereditary myopathy which is most often sex-linked autosomal recessive or rarely autosomal recessive familial pattern. Muscle weakness usually begins between ages two to five in the proximal muscles of the upper and lower extremities and is progressive, gradually resulting in multiple joint contractures and deformities, inability to ambulate, and dependence in activities of daily living.
Clinical findings, serum enzyme studies, electromyographic examination, and muscle biopsy are helpful in establishing the diagnosis, though sometimes it is difficult to differentiate Duchenne type from other types of progressive muscular dystrophy or from some neuropathic conditions of muscle.
Electromyographic findings in fifteen patients were illustrated and discussed. Appropriate therapeutic exercises adapted specifically to each stage of the disability are recommened to prolong the period of ambulation and upright posture and to provide maximum function in activities of daily living for these patients within their limits.
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